Radiological Findings in Persistent Müllerian Duct Syndrome: Case Report and Review of Literature.
نویسندگان
چکیده
This case involved a 36-year-old adult male who presented with an unusual inguinal hernia in which the uterus and fallopian tubes were identified as contents of the inguinal hernia sac. These findings reflected a rare autosomal recessive developmental syndrome known as PMDS (persistent Müllerian duct syndrome). The diagnosis was established and confirmed via radiological-mainly MRI-investigation.
منابع مشابه
Herlyn Werner Wunderlich Syndrome with Hematocolpos: An Unusual Case Report of Full Diagnostic Approach and Treatment
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متن کاملگزارش یک مورد نادر بیماری مادرزادی: Persistent Mullerian Duct Syndrome (PMDS) در یک آقای 71 ساله
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Persistent Mullerian duct syndrome is a rare form of internal male pseudohermaphroditism, in which Mullerian duct derivatives (uterus and fallopian tubes) are present in a genotypic (46XY) and phenotypic male. Over 150 cases have been reported, mainly from outside the African setting. This article presents an unexpected case encountered in an African setting. Handicaps in the management were un...
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ورودعنوان ژورنال:
- Journal of radiology case reports
دوره 11 3 شماره
صفحات -
تاریخ انتشار 2017